A nurse is caring for a child who has sickle cell disease What nursing interventions

Review

Nursing management of children with sickle cell disease: an update

D Gribbons et al. J Pediatr Nurs. 1995 Aug.

Abstract

This article reviews current trends in managing children with sickle cell disease (SCD). The pathophysiology, medical and nursing management, and complications of SCD are discussed. Current trends and research findings related to improving the prognosis of children with SCD are offered. The importance of the nurse's role in educating the family about the disease process and clinical interventions to prevent or manage complications are stressed. Lastly, a nursing care plan is offered which focuses on pertinent nursing diagnosis.

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This article reviews current trends in managing children with sickle cell disease (SCD). The pathophysiology, medical and nursing management, and complications of SCD are discussed. Current trends and research findings related to improving the prognosis of children with SCD are offered. The importance of the nurse's role in educating the family about the disease process and clinical interventions to prevent or manage complications are stressed. Lastly, a nursing care plan is offered which focuses on pertinent nursing diagnosis.

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References

    • Al-Momen A.

    Recombinant human erythropoietin induced rapid healing of a chronic leg ulcer in a patient with sickle cell disease.

    Acta Haematologica. 1991; 86: 46-48

    • Scopus (35)
    • PubMed
    • Crossref
    • Google Scholar

    • Andrews L.B.

    Issues to be considered: Overview of legal issues.

    Pediatrics. 1989; 83: 886-889

    • Google Scholar

    • Baumgartner F.
    • Klein S.

    The presentation and management of the acute abdomen in the patient with sickle-cell anemia.

    The American Surgeon. 1989; 55: 660-664

    • PubMed
    • Google Scholar

    • Beutler E.

    Bone morrow transplantation for sickle cell anemia: Summarizing comments.

    Seminars in Hematology. 1991; 28: 263-267

    • PubMed
    • Google Scholar

    • Bhatt-Mehta V.
    • Rosen D.

    Management of acute pain in children.

    Clinical Pharmacy. 1991; 10: 667-685

    • PubMed
    • Google Scholar

    • Bowman J.E.

    Legal and ethical issues in newborn screening.

    Pediatrics. 1989; 83: 894-896

    • Google Scholar

    • Bray G.
    • Muenz L.
    • Makris N.
    • Lesin L.

    Assessing the clinical severity in children with sickle cell disease.

    The American Journal of Pediatric Hematology & Oncology. 1994; 16: 50-54

    • PubMed
    • Google Scholar

    • Burlew A.K.
    • Evans R.
    • Oler C.

    The impact of a child with sickle cell disease on family dynamics.

    Annals of the New York Academy of Science. 1989; 565: 161-171

    • Scopus (52)
    • PubMed
    • Crossref
    • Google Scholar

    • Charache S.

    Hydroxyurea as treatment for sickle cell anemia.

    Hematology/Oncology Clinics of North America. 1991; 5: 571-580

    • PubMed
    • Google Scholar

    • Charache S.
    • Dover G.
    • Moore R.
    • Eckert S.
    • Ballas S.
    • Koshy M.
    • Milner P.
    • Orringer E.
    • Phillips G.
    • Platt O.
    • Thomas G.

    Hydroxyurea: Effects on hemoglobin F production in patients with sickle cell anemia.

    Blood. 1992; 79: 2555-2565

    • PubMed
    • Google Scholar

    • Charache S.
    • Lubin B.
    • Reid C.

    Management and therapy of sickle cell disease.

    US Dept of Health and Human Resources, Public Health Service, Washington, DC1991

    • Google Scholar

    • Cohen A.
    • Martin M.
    • Sibler J.
    • Kim H.
    • Ohene-Frempong K.
    • Schwartz E.

    A modified transfusion program for prevention of stroke in sickle cell disease.

    Blood. 1992; 79: 1657-1661

    • PubMed
    • Google Scholar

    • Cole T.B.
    • Sprinkles R.H.
    • Smith S.J.
    • Buchanan G.R.

    Intravenous narcotic therapy for children with severe sickle cell crisis in pain.

    American Journal of Diseases of Childhood. 1986; 140: 1255-1259

    • PubMed
    • Google Scholar

    • Dabrow M.
    • Wilkins J.

    Hematologic emergencies: Management of transfusion reactions and crises in sickle cell disease.

    Postgraduate Medicine. 1993; 93: 183-190

    • PubMed
    • Google Scholar

    • Davies S.
    • Brozovic M.

    The presentation, management and prophylaxis of sickle cell disease.

    Blood Reviews. 1989; 3: 29-44

    • Scopus (40)
    • PubMed
    • Abstract
    • Full Text PDF
    • Google Scholar

    • Dilworth-Anderson P.

    Family structure and intervention strategies.

    Annals of the New York Academy of Science. 1989; 565: 187-188

    • Scopus (3)
    • Crossref
    • Google Scholar

    • Earles A.

    Nursing perspective.

    Pediatrics. 1989; 83: 901-902

    • PubMed
    • Google Scholar

  1. Earles A. Lessing S. Vichinsky E. A parents' handbook for sickle cell disease: Part II, Six to Eighteen Years of Age. State of California Department of Health Services, Genetic Disease Branch, Sacramento, CA1993

    • Google Scholar

    • Evans J.P.

    Practical management of sickle cell disease.

    Archives of Disease in Childhood. 1989; 64: 1748-1751

    • Scopus (3)
    • PubMed
    • Crossref
    • Google Scholar

    • Fabry M.
    • Kaul D.

    Sickle cell-vaso-occlusion.

    Hematology/Oncology Clinics of North America. 1991; 5: 375-394

    • PubMed
    • Google Scholar

    • Ferster A.
    • DeValck C.
    • Azzi N.
    • Fondu P.
    • Toppet M.
    • Sariban E.

    Bone marrow transplantation for severe sickle cell anaemia.

    British Journal of Haematology. 1992; 80: 102-105

    • Scopus (44)
    • PubMed
    • Crossref
    • Google Scholar

    • Fischel-Ghodsian N.

    Prenatal diagnosis of hemoglobinopathies.

    Clinics in Pennatology. 1990; 17: 811-827

    • PubMed
    • Google Scholar

    • France-Dawson M.

    Sickle cell disease: Implications for nursing care.

    Journal of Advanced Nursing. 1986; 11: 729-737

    • Scopus (5)
    • PubMed
    • Crossref
    • Google Scholar

    • Gaukroger P.

    Paediatric analgesia, which drug, which dose?.

    Drugs. 1991; 41: 52-59

    • Scopus (27)
    • PubMed
    • Crossref
    • Google Scholar

    • Gaston M.
    • Verter J.
    • Woods G.
    • Pegelow C.
    • Kelleher J.
    • Presbury G.
    • Zarkowsky H.
    • Vichinsky E.
    • Iyer R.
    • Lobel J.
    • Diamond S.
    • Holbrook T.
    • Gill F.
    • Ritchey K.
    • Falletta J.

    Prophylaxis with oral penicillin in children with sickle cell anemia.

    The New England Journal of Medicine. 1986; 314: 1593-1599

    • Scopus (921)
    • PubMed
    • Crossref
    • Google Scholar

    • Gillespie J.
    • Morton N.

    Patient-controlled analgesia for children: A review.

    Pediatric Anaesthesia. 1992; 2: 51-59

    • Scopus (29)
    • Crossref
    • Google Scholar

    • Goldberg M.A.
    • Brugnara C.
    • Dover G.J.
    • Schapira L.
    • Charache S.
    • Bunn H.F.

    Treatment of sickle cell anemia with hydroxyurea and erythropoietin.

    The New England Journal of Medicine. 1990; 323: 366

    • Scopus (159)
    • PubMed
    • Crossref
    • Google Scholar

    • Goodman E.

    Use of ketorolac in sickle cell disease and vaso-occlusive crisis.

    The Lancet. 1991; 338: 641-642

    • Scopus (19)
    • PubMed
    • Abstract
    • Google Scholar

    • Gradolf B.

    Sickle cell anemia in children.

    Issues in Comprehensive Pediatric Nursing. 1983; 6: 295-306

    • Scopus (3)
    • PubMed
    • Crossref
    • Google Scholar

    • Haynes J.
    • Kirkpatrick M.

    The acute chest syndrome of sickle cell disease.

    The American Journal of the Medical Sciences. 1993; 305: 326-330

    • Scopus (33)
    • PubMed
    • Crossref
    • Google Scholar

    • Hernandez S.

    Social work perspective.

    Pediatrics. 1989; 83: 903-905

    • PubMed
    • Google Scholar

    • Ives T.J.
    • Guerra M.F.

    Constant morphine infusion for severe sickle cell crisis pain.

    Drug Intelligence and Clinical Pharmacy. 1987, July/August; 21: 625-626

    • PubMed
    • Google Scholar

    • Kaufman R.

    Hydroxyurea: Specific therapy for sickle cell anemia?.

    The Journal of the American Society of Hematology. 1992; 79: 2503-2506

    • Google Scholar

    • Kinney T.R.
    • Ware R.

    Advances in the management of sickle cell disease.

    Pediatric Consult. 1988; 7: 1-7

    • Google Scholar

    • Lassen K.
    • Epstein-Stiles M.
    • Olson G.L.

    Ketorolac: A new parenteral nonsteroidal anti-inflammatory drug for postoperative pain management.

    Journal of Post Anesthesia Nursing. 1992; 7: 238-242

    • PubMed
    • Google Scholar

  2. Lessing S. Vichinsky E. A parents' handbook for sickle cell disease, part 1. State of California Department of Health Services, Genetic Disease Branch, Sacramento, CA1990

    • Google Scholar

    • Lester L.A.
    • Sodt P.C.
    • Hutcheon N.
    • Arcilla R.

    Cardiac abnormalities in children with sickle cell anemia.

    Chest. 1990; 98: 1169-1174

    • Scopus (92)
    • PubMed
    • Crossref
    • Google Scholar

    • Lisak M.

    Sickle cell disease.

    in: Jackson P. Vessey J. Primary care of the child with a. Mosby Year Book, St. Louis, MO1992

    • Google Scholar

    • McPherson E.
    • Perlin E.
    • Finke H.
    • Castro O.
    • Pittman J.

    Patient-controlled analgesia in patients with sickle cell vaso-occlusive crisis.

    The American Journal of the Medical Sciences. 1990; 299: 10-12

    • Scopus (17)
    • PubMed
    • Crossref
    • Google Scholar

    • Nagel R.

    The dilemma of morrow transplantation in sickle cell anemia.

    Seminars in Hematology. 1991; 28: 233-234

    • PubMed
    • Google Scholar

    • Nienhuis A.

    Therapeutic approaches to hemoglobin switching in treatment of hemoglobinopathies.

    Annales Review of Medicine. 1992; 43: 497-516

    • Scopus (69)
    • PubMed
    • Crossref
    • Google Scholar

    • Pearson H.A.

    Sickle cell disease: Diagnosis and management in infancy and childhood.

    Pediatrics in Review. 1987; 9: 121-124

    • Scopus (10)
    • PubMed
    • Crossref
    • Google Scholar

    • Perrine S.
    • Ginder G.
    • Faller D.
    • Dover G.
    • Ikuta T.
    • Witkowska H.
    • Cai S.
    • Vichinsky E.
    • Olivieri N.

    A short term trial of butyrate to stimulate fetal-globin gene expression in the B globin disorders.

    The New England Journal of Medicine. 1993; 328: 81-86

    • Scopus (418)
    • PubMed
    • Crossref
    • Google Scholar

    • Piomelli S.

    Bone marrow transplantation in sickle cell diseases: A plea for rational approach.

    Bone Marrow Transplant. 1992; 10: 58-61

    • PubMed
    • Google Scholar

    • Platt O.
    • Brambilla D.
    • Rosse W.
    • Miller P.
    • Castro O.
    • Steinberg M.
    • Klug P.

    Mortality in sickle cell disease: Life expectancy and risk factors for early death.

    New England Journal of Medicine. 1994; 330: 1639-1644

    • Scopus (2427)
    • PubMed
    • Crossref
    • Google Scholar

    • Powars D.

    Sickle cell anemia: Bs gene cluster haplotypes as prognostic indicators of vital organ failure.

    Seminars in Hematology. 1991; 28: 202-208

    • PubMed
    • Google Scholar

    • Powars D.R.
    • Chan L.

    Is sickle cell crisis a valid measure of clinical severity in sickle cell anemia?.

    Programs in Clinical Biological Research. 1987; 240: 393-402

    • PubMed
    • Google Scholar

    • Rodgers G.

    Recent approaches to the treatment of sickle cell anemia.

    The Journal of the American Medical Association. 1991; 265: 2097-2101

    • Scopus (16)
    • Crossref
    • Google Scholar

    • Rodgers G.
    • Dover G.
    • Uyesaka N.
    • Noguchi C.
    • Schecter A.
    • Nienhus A.

    Augmentation by erythropoietin of the fetal-hemoglobin response to hydroxyurea in sickle cell disease.

    The New England Journal of Medicine. 1993; 328: 73-80

    • Scopus (219)
    • PubMed
    • Crossref
    • Google Scholar

    • Rogers Z.R.
    • Morrison R.A.
    • Vedro D.A.
    • Buchanan G.R.

    Outpatient management of febrile illness in infants and young children with sickle cell anemia.

    The Journal of Pediatrics. 1990; 117: 736-739

    • Scopus (40)
    • PubMed
    • Abstract
    • Full Text PDF
    • Google Scholar

    • Sarnaik S.
    • Merline J.
    • Bond S.

    Immunogenicity of hepatitis B vaccine in children with sickle cell anemia.

    Journal of Pediatrics. 1988; 112: 429-430

    • Scopus (7)
    • PubMed
    • Abstract
    • Full Text PDF
    • Google Scholar

    • Shapiro B.X.

    The management of pain in sickle cell disease.

    Pediatric Clinics of North America. 1989; 36: 1029-1045

    • PubMed
    • Google Scholar

    • Sullivan K.
    • Reid C.
    Introduction to a symposium on sickle cell anemia: Current results of comprehensive care and the evolving role of bone marrow transplantation. Seminars in Hematology. 28. 1991: 177-179

    • Google Scholar

    • Thomas E.

    The pros and cons of bone marrow transplantation for sickle cell anemia.

    Seminars in Hematology. 1991; 28: 260-262

    • PubMed
    • Google Scholar

    • Tsevat J.
    • Wong J.B.
    • Pauker S.G.
    • Steinberg M.H.

    Neonatal screening for sickle cell disease: A cost-effectiveness analysis.

    The Journal of Pediatrics. 1991; 118: 546-554

    • Scopus (58)
    • PubMed
    • Abstract
    • Full Text PDF
    • Google Scholar

    • Vermylen C.
    • Cornu G.

    Bone marrow transplantation for sickle cell disease: The European experience.

    The American Journal of Pediatric Hematology/Oncology. 1994; 16: 18-21

    • PubMed
    • Google Scholar

    • Vichinsky E.
    • Lubin B.

    Suggested guidelines for the treatment of children with sickle cell anemia.

    Hematology/Oncology Clinics of North America. 1987; 1: 483-498

    • PubMed
    • Google Scholar

    • Walker B.

    Public health perspective on newborn screening for hemoglobinopathies.

    Pediatrics. 1989; 83: 912

    • PubMed
    • Google Scholar

    • Wang W.C.
    • Kovnar E.H.
    • Tonkin I.L.
    • Mulhern R.K.
    • Langston J.W.
    • Day S.W.
    • Schell M.J.
    • Wilmas J.A.

    High risk of recurrent stroke after discontinuance of five to twelve years of transfusion therapy in patients with sickle cell disease.

    The Journal of Pediatrics. 1991; 118: 377-382

    • Scopus (156)
    • PubMed
    • Abstract
    • Full Text PDF
    • Google Scholar

Article Info

Identification

DOI: https://doi.org/10.1016/S0882-5963(05)80020-X

Copyright

© 1995 W.B. Saunders Company. Published by Elsevier Inc.

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